海外マルファン情報

米国マルファン症候群患者団体The Marfan Foundationからの情報を中心に、マルファン症候群や関連疾患についての海外情報を翻訳して発信します。

オンラインセミナー

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~着床前診断~

Family Planning and Pregnancy: US and Europe Perspectives 16:42-18:03 So talking just about pre-implantation genetic ??? testing on the embryo. It's usually going to be made in a dish and then it's day five or six, you can take one cell fr…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~「親」になるという選択~

Family Planning and Pregnancy: US and Europe Perspectives 16:01-16:39 So the decision to become a parent again is really a personal decision and then how you achieve this goal is very individualized based on your medical risks, your morals…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~着床前診断・出生前診断~

Family Planning and Pregnancy: US and Europe Perspectives 14:20-15:59 So changing gears and sort of talking about genetics and heritability. A bunch of people asked prior to the president the, this presentation, "what is the risk of me pas…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~β遮断薬、ACE阻害薬・ARB、ワーファリン~

Family Planning and Pregnancy: US and Europe Perspectives 10:46-14:17 In terms of meditation, the first thing I want to say is it's really important to not just stop or start a medication you should always be doing this with one of your do…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~産科の合併症~

Family Planning and Pregnancy: US and Europe Perspectives 9:56-10:43 Okay, so other people are going to be talking about risks in relation to pregnancy more of the cardiac side of things. From an obstetric standpoint there are studies that…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~妊娠前カウンセリング~

Family Planning and Pregnancy: US and Europe Perspectives 7:43-9:54 So I'm talking about preconception counseling. We're going to talk about the one baseline knowledge about your body, so sort of getting imaging before pregnancy, we're goi…

ロサルタン以外のARBの効果について

Aortic Disease Research (9/19/22) 51:42-53:41 Q: Karen, who we know, she wants to know is Valsartan as effective as Losartan in diminishing growth of the aorta. Eileen: 大動脈の拡張を抑えるという点では、バルサルタンでもロサルタンと同じくら…

大動脈疾患に関する研究報告(Science in Paris) ~IRADの論文と新ガイドライン~

Aortic Disease Research (9/19/22) 38:47-42:50 So a couple of other updates that I think are, are interesting and, and timely. The IRAD group that I have the pleasure of sharing over the last 25 years published about two weeks ago a paper i…

大動脈疾患に関する研究報告(Science in Paris) ~二尖大動脈弁~

Aortic Disease Research (9/19/22) 34:55-38:43 So bicuspid aortic valve is a very common inherent disorder of the aortic valve and a certain percentage of patients 10 to 35 percent also have an abnormal, abnormal aorta. I think it's estimat…

大動脈疾患に関する研究報告(Science in Paris) ~血管型エーラス・ダンロス症候群~

Aortic Disease Research (9/19/22) 32:19-34:52 So vascular Ehlers-Danlos represents a really important effort of the foundation and of scientists around the world and I would like to suggest that in some ways with vascular EDS we're just be…

大動脈疾患に関する研究報告(Science in Paris) ~ロイス・ディーツ症候群~

Aortic Disease Research (9/19/22) 28:04-32:15 So Loeys-Dietz syndrome, there were a number of important articles or publications or presentations at the meeting. Two that I thought were especially important. ロイス・ディーツ症候群について…

大動脈疾患に関する研究報告(Science in Paris) ~マルファン症候群~

Aortic Disease Research (9/19/22) 23:25-28:00 The Marfan syndrome presentations were numerous and, and almost too many to cite. I pulled just a couple. マルファン症候群については、多くの発表がありました。その中からいくつかご紹介します。 Th…

大動脈疾患に関する研究報告(Science in Paris) ~大動脈解離サバイバーが望んでいること~

Aortic Disease Research (9/19/22) 20:42-23:20 So, this was a very interesting analysis. Sherene Shalhub and others led a large group of patients to try to understand from patients and families, what, what are the research priorities that y…

大動脈疾患に関する研究報告(Science in Paris) ~バイオマーカー~

Aortic Disease Research (9/19/22) 16:39-20:39 So where are we with biomarkers? So biomarkers are proteins that are circulating in the blood that we would like to be able to use to either diagnose or prognosticate certain problems. バイオマ…

大動脈疾患に関する研究報告(Science in Paris) ~4DフローMRI~

Aortic Disease Research (9/19/22) 14:15-16:33 This was a study, which actually was done by one of our imagers at the University of Michigan, Nick Burris and one of the things that we've been trying to understand is if a person has an aorto…

大動脈疾患に関する研究報告(Science in Paris) ~小児の運動~

Aortic Disease Research (9/19/22) 10:20-14:10 So there were a number of studies presented in Paris which looked at a quality of life in children who have hereditary thoracic aortic disease and as you might expect in general children who ha…

大動脈の画像検査 ~CTでみる大動脈解離~

Aortic Imaging: Your Questions Answered 13:28-14:14 The other image I want to share here is how does a dissection look on CT. So this is basically what we call a snake view of the aorta, whole of the aorta. On the top is the root as you co…

大動脈の画像検査 ~造影CTでの上行大動脈の太さ計測~

Aortic Imaging: Your Questions Answered 12:15-13:27 This is a important point I want to make. How is an ascending aorta right above the root is measured? On the left here is a normal technique that's used very often where you measure the a…

大動脈の画像検査 ~CT・造影CT~

Aortic Imaging: Your Questions Answered 10:05-12:14 Then the next technique I want to show are images of thoracic aorta but remember how the tissue is looking here. This is a non-contrast CT so there is no contrast that we have administere…

大動脈の画像検査 ~TTE・TOE~

Aortic Imaging: Your Questions Answered 8:54-10:04 So here, this is where I, the most important part of that presentation is I just want to share images and go over what I'm looking at, so these are echocardiography images on patients on s…

大動脈の画像検査 ~各種画像検査についての説明~

Aortic Imaging: Your Questions Answered 7:05-8:54 With that, you know, the other thing to remember is there are different techniques available. Each has its strength and weaknesses so which to use when it becomes very important. では画像検…

大動脈の画像検査 ~大動脈の部位説明~

Aortic Imaging: Your Questions Answered 6:07-7:01 This is a cartoon showing different areas of the aorta that everybody is interested in knowing that the part that's connected to the heart, the sinus is called basically sinus of valsalva a…

大動脈の画像検査 ~はじめに~

Aortic Imaging: Your Questions Answered 4:44-6:06 Thank you for joining and I would like to thank the Marfan Foundation for giving me an opportunity to present on cardiovascular imaging, especially vascular imaging, which is very important…

大動脈手術の将来について

Advances in the Treatment of Aortic Dissection 58:00-1:00:10 Q: How do you feel about this the state of aortic surgery right now. What are you looking forward to in the future? What do patients have to look forward to? Eileen:大動脈手術の…

大動脈解離が外科手術なしで治ることがあるか?

Advances in the Treatment of Aortic Dissection 56:12-57:53 Q: Does the dissection ever heal so that surgery isn't necessary or does it stabilize, does it ever heal? Eileen: 大動脈解離が自然に治って手術が不要になったり、安定するということは…

大動脈解離手術後の画像検査について

Advances in the Treatment of Aortic Dissection 54:46-56:09 Q: And I'm on the other end, Dr. Ohman, you talked about long-term surveillance after the surgery, so how frequently with what kind of imaging, you know, what do you recommend for …

大動脈解離の前兆はあるか?

Advances in the Treatment of Aortic Dissection 53:56-54:46 Q: People want to know, I mean, they see obviously that it's better to have surgery prophylactically than emergently. Besides the size, which they would know themselves, are there …

10代の大動脈手術について

Advances in the Treatment of Aortic Dissection 52:29-53:56 Q:So I know you you both do a surgery on adults, correct? and so some people are asking about some of this information pertains to children as well. Obviously in Marfan and Loeys-D…

PEARSについて教えてください

Advances in the Treatment of Aortic Dissection 48:50-52:29 Q: I have a few questions about PEARS procedure, which we didn't talk about. So Alan, come back. I see you want to answer one of these but is there anything new on the PEARS proced…

ロイス・ディーツ症候群の血管手術において覚えておくべきこと

Advances in the Treatment of Aortic Dissection 46:57-48:47 Q: Are there different recommendations for surgery if a patient is Loeys-Dietz compared to Marfan? Eileen: ロイス・ディーツ症候群の血管手術において、マルファン症候群と比較して、特…