Pediatric Take on 2022 Adult Guidelines for Diagnosis and Treatment of Aortic Disease 2:27-3:35 Children grow, is something we know well looking at the growth chart for infants. So on the pink growth chart, there you can see, there's very …

Pediatric Take on 2022 Adult Guidelines for Diagnosis and Treatment of Aortic Disease 0:00-2:25 Hi, I'm Dr. Glenn Iannucci. I'm a Pediatric Cardiologist at Children's Healthcare of Atlanta with Emory University and I run our aorta and Vasc…

Vascular Surgery 19:52-21:09 Q: Does Loeys-Dietz change if you go through the femoral artery or open embolization due to more fragile tissue? LDSでは組織が脆弱ということなので、大腿動脈からコイル塞栓術を行う場合、処置に違いはあるのでしょう…

Vascular Surgery 17:35-18:51 Common iliac artery aneurysms you heard I've said it's if we're going to see it in, in people with Marfan syndrome we will see frequently common iliac artery aneurysms and then again very frequently we'll see t…

Vascular Surgery 16:38-17:34 The Celiac artery aneurysms and dissections again frequently these are present in our population and most of them can be managed medically and on rare circumstances we do embolization for those, next slide. 腹…

Vascular Surgery 15:09-16:34 There are circumstances in which there are aneurysms like I said and these require an open repair and like I said in extreme circumstances is a case of a woman who had embolization of her carotid artery, so tha…

Vascular Surgery 14:42-15:07 This is important in terms of data. The question always comes up if we want to use aspirin or anti-platelet therapy versus anticoagulation that's coumadin in carotid artery dissections or vertebral artery disse…

Vascular Surgery 13:21-14:40 So I'm going to run through quickly. These are again the arterial tree, if you will from top to bottom so we're just going to go through and give you examples of how they're managed, next slide. では、動脈全体…

Vascular Surgery 12:15-13:18 And this is just a comment on access sites because as I said you go through the femoral artery when we do these and so we have to be careful with the way we close the femoral artery so that we don't have pseudo…

Vascular Surgery 10:10-13:18 So when we talk about endovascular repair you've heard two terms. You've heard embolization and you've heard stenting but basically these are what we call minimally invasive procedures. We perform them through …

Vascular Surgery 9:44-10:07 Medical management. Just touching on that very briefly that if there's hypertension we want to treat it. If somebody smokes they need to quit smoking because smoking is one of the most detrimental things you can…

Vascular Surgery 8:50-9:42 I do follow people with vascular surveillance. You heard about that from Dr. Young who talked about the surveillance for the aortic root. Similarly for the rest of the vasculature I like to get a baseline CT scan…

Vascular Surgery 7:06-8:49 So aortic aneurysms, this is specifically for abdominal aortic aneurysms, not, not ascending you've heard a lot about the ascending and root aneurysm thresholds but this is for abdominal aortic aneurysms and you …

Vascular Surgery 5:24-7:04 So in terms of repair principles we do know that most aneurysms and dissections can be managed non-operatively and I think this is a very important concept to make because when people hear that they have a dissec…

動脈瘤・解離の管理Vascular Surgery 3:29-5:23 You've seen this picture. This is from Gustavo Oderich's paper where a few years ago he talked about the distribution of arteriopathy in vascular EDS and then on the right hand side is our paper…

Vascular Surgery 1:55-3:27 Dissection on the other hand is different. Dissection means that there's a tear in the wall of the artery or the aorta and blood then flows between those layers and what that does is then as you can see in the pi…

Vascular Surgery 0:18-1:52 Basically my goal for the audience here is to learn the difference between aneurysms and dissections because frequently people can confuse the two. I will show you the distribution of the arterial pathology in va…

LDS Guidelines: Then vs. Now 1:21:13-1:24:12 Q:Last question for you, Dr Dietz. In terms of exercising what are your suggestions in terms of kind of like heart rate recommendations or kind of what guidelines say and how you think or feel a…

LDS Guidelines: Then vs. Now 1:17:49-1:20:45 Q:If anyone has any thoughts on just osteoporosis or joint degradation we might see in Loeys-Dietz syndrome and any type of supplement in terms of calcium or things like that? LDSで見られる骨粗…

LDS Guidelines: Then vs. Now 1:16:18-1:17:26 Q:There are few questions about the use of inhalers and flovent and albuterol, which is kind of in your realm, too. Can you address that? フルタイドやサルブタモールなどの吸入ステロイドについて、…

LDS Guidelines: Then vs. Now 1:13:55-1:16:15 Q:Any evidence of prevalence of autoimmune conditions with Loeys-Dietz syndrome like rheumatoid arthritis or other immunity, I guess, autoimmune conditions? LDSでは、関節リウマチのような自己免疫…

LDS Guidelines: Then vs. Now 1:11:03-1:13:52 Q:Any correlation or conversation about POTS in Loeys-Dietz syndrome? POTSとLDSは関連がありますか？ A:Yeah, so POTS stands for Postural Orthostatic Tachycardia Syndrome. Basically what it's desc…

LDS Guidelines: Then vs. Now 1:09:38-1:11:01 Q:Any thoughts on neuropathy in Loeys-Dietz syndrome and/or, you know, how they impact pain management? LDSでの神経障害について教えてください。痛みの管理法に影響はあるのでしょうか？ A:Yeah, so I…

LDS Guidelines: Then vs. Now 1:08:02-1:09:32 Q:Is there any precautions with arterial line insertion for anesthesia and the risk of arterial dissection in Loeys-Dietz patients, so maybe also like catheter procedures. LDSでは、血管に管を入…

LDS Guidelines: Then vs. Now 1:04:25-1:07:52 Q:Kind of along the lines of medication in that first question or that first slide we were talking about non-penetrance. Can you talk a little bit just about your thought process when you're cou…

LDS Guidelines: Then vs. Now 1:01:25-1:04:24 Q:One of the questions, I'll just kind of start picking some, is about you talked about the meta-analysis which was awesome and then you touched upon adding a beta blocker. Can you just let us k…

LDS Guidelines: Then vs. Now 58:37-59:43 From a lung, pulmonary perspective we know, do know that there is restrictive lung disease, that sleep apnea may be underdiagnosed in our population, so again in terms of like general fatigue and pe…

LDS Guidelines: Then vs. Now 57:36-58:37 In terms of eye disease we do see retinal detachment. I know some of your questions are, what's common, what's not, what's rare, what do I have to be worried about. 眼の疾患については、一般的な眼の…

LDS Guidelines: Then vs. Now 54:34-57:35 In 2014 we did talk about kind of neurological issues. In the first reports of Loeys-Dietz syndrome we had some cases of individuals with intellectual disability, however, we think this is really re…

LDS Guidelines: Then vs. Now 52:45-54:31 Great and then we just want to end with a few slides of kind of like all the other stuff and so we know that in patients with Loeys-Dietz syndrome there can be dental anomalies that can include clea…