Medical Therapy in the Pediatric Patient 0:00-4:53 Hi, I'm Dr. Glenn Iannucci. I'm a pediatric cardiologist at Children's Healthcare of Atlanta and director of the aorta and vascular program and on behalf of the GenTAC alliance I'll be pre…
Pediatric Take on 2022 Adult Guidelines for Diagnosis and Treatment of Aortic Disease 7:22-8:20 Another point that was highlighted in the 2022 guidelines was that we should try to remember the family, so aortic disease is a progressive con…
Pediatric Take on 2022 Adult Guidelines for Diagnosis and Treatment of Aortic Disease 5:50-7:22 One of the other points that was highlighted in the 2022 guidelines were the recommendation that patients with stable aortic disease be referre…
Pediatric Take on 2022 Adult Guidelines for Diagnosis and Treatment of Aortic Disease 5:10-5:49 Because some degree of growth of the aorta is normal for children we must use caution when reviewing the 2022 AHA guidelines that point out tha…
Pediatric Take on 2022 Adult Guidelines for Diagnosis and Treatment of Aortic Disease 3:36-5:03 So as children are growing one of the questions that often comes up is "Is my aortic growth physiologic or pathologic?" and by physiologic grow…
Pediatric Take on 2022 Adult Guidelines for Diagnosis and Treatment of Aortic Disease 2:27-3:35 Children grow, is something we know well looking at the growth chart for infants. So on the pink growth chart, there you can see, there's very …
Pediatric Take on 2022 Adult Guidelines for Diagnosis and Treatment of Aortic Disease 0:00-2:25 Hi, I'm Dr. Glenn Iannucci. I'm a Pediatric Cardiologist at Children's Healthcare of Atlanta with Emory University and I run our aorta and Vasc…
Should I tell people that I have Marfan syndrome? Often children with Marfan syndrome feel the need to try to hide their condition. They don't want to admit to anyone else that they are different even though often it's quite obvious that t…
Vascular Surgery 19:52-21:09 Q: Does Loeys-Dietz change if you go through the femoral artery or open embolization due to more fragile tissue? LDSでは組織が脆弱ということなので、大腿動脈からコイル塞栓術を行う場合、処置に違いはあるのでしょう…
Vascular Surgery 17:35-18:51 Common iliac artery aneurysms you heard I've said it's if we're going to see it in, in people with Marfan syndrome we will see frequently common iliac artery aneurysms and then again very frequently we'll see t…
Vascular Surgery 16:38-17:34 The Celiac artery aneurysms and dissections again frequently these are present in our population and most of them can be managed medically and on rare circumstances we do embolization for those, next slide. 腹…
Vascular Surgery 15:09-16:34 There are circumstances in which there are aneurysms like I said and these require an open repair and like I said in extreme circumstances is a case of a woman who had embolization of her carotid artery, so tha…
Vascular Surgery 14:42-15:07 This is important in terms of data. The question always comes up if we want to use aspirin or anti-platelet therapy versus anticoagulation that's coumadin in carotid artery dissections or vertebral artery disse…
Vascular Surgery 13:21-14:40 So I'm going to run through quickly. These are again the arterial tree, if you will from top to bottom so we're just going to go through and give you examples of how they're managed, next slide. では、動脈全体…
Vascular Surgery 12:15-13:18 And this is just a comment on access sites because as I said you go through the femoral artery when we do these and so we have to be careful with the way we close the femoral artery so that we don't have pseudo…
Vascular Surgery 10:10-13:18 So when we talk about endovascular repair you've heard two terms. You've heard embolization and you've heard stenting but basically these are what we call minimally invasive procedures. We perform them through …
Vascular Surgery 9:44-10:07 Medical management. Just touching on that very briefly that if there's hypertension we want to treat it. If somebody smokes they need to quit smoking because smoking is one of the most detrimental things you can…
Vascular Surgery 8:50-9:42 I do follow people with vascular surveillance. You heard about that from Dr. Young who talked about the surveillance for the aortic root. Similarly for the rest of the vasculature I like to get a baseline CT scan…
Vascular Surgery 7:06-8:49 So aortic aneurysms, this is specifically for abdominal aortic aneurysms, not, not ascending you've heard a lot about the ascending and root aneurysm thresholds but this is for abdominal aortic aneurysms and you …
How can parents advocate for their child in school? When I was talking with the teenagers at the conference for two years straight two years in a row, the thing with PE was such a big issue for girls and boys. It was almost across the boar…
Vascular Surgery 5:24-7:04 So in terms of repair principles we do know that most aneurysms and dissections can be managed non-operatively and I think this is a very important concept to make because when people hear that they have a dissec…
動脈瘤・解離の管理Vascular Surgery 3:29-5:23 You've seen this picture. This is from Gustavo Oderich's paper where a few years ago he talked about the distribution of arteriopathy in vascular EDS and then on the right hand side is our paper…
Vascular Surgery 1:55-3:27 Dissection on the other hand is different. Dissection means that there's a tear in the wall of the artery or the aorta and blood then flows between those layers and what that does is then as you can see in the pi…
Vascular Surgery 0:18-1:52 Basically my goal for the audience here is to learn the difference between aneurysms and dissections because frequently people can confuse the two. I will show you the distribution of the arterial pathology in va…
LDS Guidelines: Then vs. Now 1:21:13-1:24:12 Q:Last question for you, Dr Dietz. In terms of exercising what are your suggestions in terms of kind of like heart rate recommendations or kind of what guidelines say and how you think or feel a…
LDS Guidelines: Then vs. Now 1:17:49-1:20:45 Q:If anyone has any thoughts on just osteoporosis or joint degradation we might see in Loeys-Dietz syndrome and any type of supplement in terms of calcium or things like that? LDSで見られる骨粗…
LDS Guidelines: Then vs. Now 1:16:18-1:17:26 Q:There are few questions about the use of inhalers and flovent and albuterol, which is kind of in your realm, too. Can you address that? フルタイドやサルブタモールなどの吸入ステロイドについて、…
LDS Guidelines: Then vs. Now 1:13:55-1:16:15 Q:Any evidence of prevalence of autoimmune conditions with Loeys-Dietz syndrome like rheumatoid arthritis or other immunity, I guess, autoimmune conditions? LDSでは、関節リウマチのような自己免疫…
LDS Guidelines: Then vs. Now 1:11:03-1:13:52 Q:Any correlation or conversation about POTS in Loeys-Dietz syndrome? POTSとLDSは関連がありますか？ A:Yeah, so POTS stands for Postural Orthostatic Tachycardia Syndrome. Basically what it's desc…
LDS Guidelines: Then vs. Now 1:09:38-1:11:01 Q:Any thoughts on neuropathy in Loeys-Dietz syndrome and/or, you know, how they impact pain management? LDSでの神経障害について教えてください。痛みの管理法に影響はあるのでしょうか？ A:Yeah, so I…
