Pediatric Gastrointestinal Issues in LDS (August 27, 2020) E3 Summit
58:43-1:01:09
Q:
Could you speak to the effects of connect, connective tissue disorders on the pelvic floor? This person specifically asked about Marfan but maybe broadly or Loeys-Dietz, Marfan...
結合組織疾患が骨盤底に与える影響について解説をお願いします。質問者の方はMarfanの方ですが、LDSにも当てはまるのではないかと思います。
A:
So with connective tissue disorders and then specifically everything I'm saying is also generalizable to Marfan, so this been, this has been looked at in Marfan's as well. We haven't looked at pelvic floor sort of as a scientific research question but certainly from our clinical experience we, we see that as well.
結合組織疾患に関し、特に私が述べていることについては、全てMarfan症候群にも当てはまります。この質問については、Marfan症候群でも調べられています。骨盤底は医学的な研究の対象となっているわけではないのですが、患者さんを診察している経験から、結合組織疾患により影響を受けることははっきりとしています。
So the pelvic floor is a collection of tissues and muscles in the the base of the pelvis that sort of they do have a significant participation in having a bowel movement and also in terms of controlling urine and things like that.
骨盤底は骨盤下部にある組織や筋肉が集まった部位で、排便や排尿に重要な役割を果たしています。
So we do see that there is a significant percentage of people with Marfan syndrome who have problems with the pelvic floor muscles and having it be weak, which can lead to difficulty having a bowel movement, it can lead to some urinary incontinence, it can lead to fecal incontinence, so yes, we do see it.
骨盤底筋に問題のあるMarfan患者さんの割合は非常に高いことがわかっています。つまり筋肉が弱いということですが、それによって排便困難、尿や便の失禁が起きることがあります。
It can be addressed so what you're really looking for to address it is pelvic floor physical therapy, which is very available. It's in a lot of places. You know, typically you'll see them mostly involved with so, you know, after they've had several children a lot of women have problems with their pelvic floor muscles and they do need some pelvic floor physical therapy.
治療は骨盤底理学療法です。多くの施設でこの治療を受けられます。出産回数の多い女性では、骨盤底筋に問題が生じますので、そうした方々が主にこの治療を受けています。
But all of the techniques that they use apply to connective tissue disorders so, you know, for younger kids what I tell people is, you know, these places are easy to find, you know, but they're used to treating postmenopausal women. So you, you need, you know, just when you make contact with them is, you know, "Hey, this is, this is for a younger person." You know, and the larger groups certainly have experience with that and the ability to do it because it's, it's all the same exercises and it's all the same interventions
ですが、この治療法は結合組織疾患の患者さんにもそのまま使うことができます。やり方は同じなので、この治療法に精通している医療施設は多くあります。
And again it's what you're working on is strengthening those pelvic floor muscles and that can really help with both pelvic floor dyssenergy and with this pelvic floor weakness, pelvic floor prolapse that can develop in connective tissue disorders.
この治療で骨盤底筋を鍛えることにより、骨盤底の共同運動障害や骨盤底筋の筋力低下、骨盤底骨盤臓器脱といった結合組織疾患で生じやすい問題を改善できます。
The Marfan Foundation did not participate in the translation of these materials and does not in any way endorse them. If you are interested in this topic, please refer to our website, Marfan.org, for materials approved by our Professional Advisory Board.
The Marfan Foundation は、当翻訳には関与しておらず、翻訳内容に関してはいかなる承認も行っておりません。このトピックに興味をお持ちの方は、Marfan.org にアクセスし、当協会の専門家から成る諮問委員会が承認した内容をご参照ください。
