Lung Issues in Marfan Syndrome
3:58-5:32
And so, I start with this triangle because this slide focuses on the most common symptom that patients with Marfan syndrome develop and that can possibly involve the lung and that is shortness of breath.
では、この三角形をご覧ください。このスライドでは、マルファン患者さんに最も多く認められる肺の症状である息切れに焦点を当てて説明します。
Most of the time physicians are very, very eager to rule out cardiac issues and so we're concerned the valvular heart disease, the rhythm disturbances, and cardiomyopathy, which is really kind of a weakened heart muscle, all of which can occur in Marfan syndrome and some physicians even kind of address the possibility of deconditioning which is also quite common in Marfan syndrome and maybe somewhat accelerated in persons who have Marfan syndrome who are sedentary compared to the general population.
大抵の場合、医師は心臓の病気を懸命に除外しようとします。我々医師は、マルファン症候群の患者さんによくみられる、心臓弁膜症や心律動障害、心筋症（心筋の異常により心機能が障害される疾患）を疑います。また、身体機能低下を疑う医師もいます。この症状もマルファン患者さんでは一般的で、特に座りがちな方では一般人口と比較して幾分病状が進行しやすいようです。
But the, the issue in the system that is often overlooked is the possibility that the shortness of breath is caused by lung disease and there are many lung impairments that we see in Marfan syndrome and these include chest wall deformity, deformities, respiratory muscle weakness, enlarged air spaces or blebs and emphysema formation, pneumothorax, sleep apnea syndrome, and also asthma and pulmonary hypertension.
ですが、息切れの原因として見落とされやすいのが肺の疾患です。マルファン患者さんでは、多くの肺疾患がみられます。例えば、胸壁奇形、呼吸筋力低下、気腔拡張やブレブ形成、肺気腫、気胸、睡眠時無呼吸症候群、喘息、肺高血圧などです。
But, in the interest of time, I'm not going to be able to talk in depth about asthma and pulmonary hypertension, but if you have questions related to those impairments please submit the questions and I will address them during our question and answer portion.
時間の都合で、喘息と肺高血圧については深くお話できませんが、これらについては、Q&Aコーナーで質問を受け付けます。
The Marfan Foundation did not participate in the translation of these materials and does not in any way endorse them. If you are interested in this topic, please refer to our website, Marfan.org, for materials approved by our Professional Advisory Board.
The Marfan Foundationは、当翻訳には関与しておらず、翻訳内容に関してはいかなる承認も行っておりません。このトピックに興味をお持ちの方は、Marfan.orgにアクセスし、当協会の専門家から成る諮問委員会が承認した内容をご参照ください。
