海外マルファン情報

米国マルファン症候群患者団体The Marfan Foundationからの情報を中心に、マルファン症候群や関連疾患についての海外情報を翻訳して発信します。

Entries from 2022-08-01 to 1 month

ロイス・ディーツ症候群の血管手術において覚えておくべきこと

Advances in the Treatment of Aortic Dissection 46:57-48:47 Q: Are there different recommendations for surgery if a patient is Loeys-Dietz compared to Marfan? Eileen: ロイス・ディーツ症候群の血管手術において、マルファン症候群と比較して、特…

ステントグラフト治療が結合組織疾患患者に向かない理由

Advances in the Treatment of Aortic Dissection 44:03-46:55 Q:Dr. Ohman, you mentioned, you said that but the endovascular repair not being for connective tissue disorder patients. There's so many questions about that. Can you explain why a…

AATS 2021 の最大の変更点について

Advances in the Treatment of Aortic Dissection 42:25-44:02 Q:Let's start with a question for Dr. Moon. You mentioned the new AATS guidelines.What, what were the, were big three big changes that came out of that? Eileen: では、最初の質問はM…

大動脈解離の治療における進展 ~B型解離のまとめ~

Advances in the Treatment of Aortic Dissection 40:40-42:15 So where are we going in the future and what, if you take away four things from this talk what should it be? ではまとめです。このスライドにある4つのポイントを覚えておいていただきた…

大動脈解離の治療における進展 ~血管内治療(マルファン関連疾患患者の場合)~

Advances in the Treatment of Aortic Dissection 37:01-40:39 Most of the experiences in the literature are single study or single center institution reports with a handful, maybe, two dozen at best and you can see for patients in both dissec…

大動脈解離の治療における進展 ~血管内治療(一般患者の場合)~

Advances in the Treatment of Aortic Dissection 35:32-37:01 And why is that? So endovascular repair sounds so much better than a big open operation. It's two needle pokes in the groin, you're watched in the ICU but we really have to ask, go…

大動脈解離の治療における進展 ~選択的修復における標準治療(GenTACの声明)~

Advances in the Treatment of Aortic Dissection 34:04-35:31 And so I have to be clear. GenTAC has a statement and, and this is true for patients who are stable and are undergoing elective repair open surgery remains the gold standard. GenTA…

大動脈解離の治療における進展 ~B型解離の手術タイミング~

Advances in the Treatment of Aortic Dissection 31:53-34:04 So when do we make the decision to go to the operating room? If it's an acute, malperfusion issue with solely a type B and they're relatively stable I want to be very clear ―― the …

大動脈解離の治療における進展 ~薬物療法~

Advances in the Treatment of Aortic Dissection 31:12-31:52 Medication remains the gold standard. Nothing has changed. That's true for type A. That's true for type B as well as residual dissections after type A repair. 薬物療法は大動脈解離…

大動脈解離の治療における進展 ~B型解離と妊娠・出産~

Advances in the Treatment of Aortic Dissection 29:12-31:11 What about pregnancy? This is a very common question and we presume that these females who are pregnant are at a higher risk due to the physiologic changes. The heart has to work h…

大動脈解離の治療における進展 ~プレシジョン・メディスンに向けて~

Advances in the Treatment of Aortic Dissection 26:58-29:11 So there's this question of the Phenotype-Genotype interplay. We know that certain gene mutations within the Marfan family are associated with a higher rate of ectopia lentis or sk…

大動脈解離の治療における進展 ~B型解離のリスク因子~

Advances in the Treatment of Aortic Dissection 24:36-26:58 But ultimately what does all of this mean for you, for patients who do have a diagnosis or a suggestion of a genetically triggered aortopathy? B型解離の概要は先程述べた通りですが、…

大動脈解離の治療における進展 ~B型解離の概要~

Advances in the Treatment of Aortic Dissection 22:12-24:35 My name is Wesley Ohman and it's honestly an honor to be paired up with Dr. Moon, who taught me so much about what I'm going to be talking about in terms of management of type B ao…

大動脈解離の治療における進展 ~A型解離治療のまとめ~

Advances in the Treatment of Aortic Dissection 21:01-21:59 So early diagnosis and institution of definitive therapy is the key. A型解離では、早期発見と根本的な治療のできる医療施設で治療を受けられるかどうかがカギとなります。 Surgical treatm…

大動脈解離の治療における進展 ~術後の血圧管理~

Advances in the Treatment of Aortic Dissection 19:51-21:00 These are the couple of most important things. I've got a good friend, Joe Bavaria, who works at the University of Pennsylvania. When we publish these data he told me he keeps this…

大動脈解離の治療における進展 ~自己弁温存手術の転帰:ワシントン大学の場合~

Advances in the Treatment of Aortic Dissection 18:36-19:50 At Washington University we've done, we just presented our series at the last surgical meeting of 177 of these patients who had valve sparing procedures, very young patients averag…

大動脈解離の治療における進展 ~外科手術の術式~

Advances in the Treatment of Aortic Dissection 17:14-18:35 So here let's look at the options for repair. Supracommissural replacement, that's an ascending aortic replacement is number, is letter a and that's just a classic repair. We repai…

大動脈解離の治療における進展 ~大動脈解離の修復手術で考慮すべきこと~

Advances in the Treatment of Aortic Dissection 16:33-17:13 So we need to talk about cannulation. That's how we put somebody on the heart-lung machine whether we do in a vessel near your head or a vessel in your leg. These are all important…

大動脈解離の治療における進展 ~治療法別の院内死亡率(IRAD)~

Advances in the Treatment of Aortic Dissection 15:35-16:11 So the IRAD database is a database all over the world that puts all their data into one spot and looks at results. では、IRADからわかっていることをご紹介します。IRADとは、急性大動…

大動脈解離の治療における進展 ~A型解離の手術適応と手術の目的~

Advances in the Treatment of Aortic Dissection 14:06-15:34 So when do we treat an acute dissection? Well, any patient who's deemed survivable and so it used to be that "Oh, if you're over 80 you don't get treated," but that's just not true…