海外マルファン情報

米国マルファン症候群患者団体The Marfan Foundationからの情報を中心に、マルファン症候群や関連疾患についての海外情報を翻訳して発信します。

Entries from 2023-10-01 to 1 month

動脈瘤・解離の管理 ~動脈全体の画像検査~

Vascular Surgery 8:50-9:42 I do follow people with vascular surveillance. You heard about that from Dr. Young who talked about the surveillance for the aortic root. Similarly for the rest of the vasculature I like to get a baseline CT scan…

動脈瘤・解離の管理 ~腹部大動脈瘤・内臓動脈瘤の修復サイズ~

Vascular Surgery 7:06-8:49 So aortic aneurysms, this is specifically for abdominal aortic aneurysms, not, not ascending you've heard a lot about the ascending and root aneurysm thresholds but this is for abdominal aortic aneurysms and you …

学校生活に関する座談会

How can parents advocate for their child in school? When I was talking with the teenagers at the conference for two years straight two years in a row, the thing with PE was such a big issue for girls and boys. It was almost across the boar…

動脈瘤・解離の管理 ~治療法~

Vascular Surgery 5:24-7:04 So in terms of repair principles we do know that most aneurysms and dissections can be managed non-operatively and I think this is a very important concept to make because when people hear that they have a dissec…

動脈瘤・解離の管理 ~vEDS/LDS/MFSでの動脈疾患分布~

動脈瘤・解離の管理Vascular Surgery 3:29-5:23 You've seen this picture. This is from Gustavo Oderich's paper where a few years ago he talked about the distribution of arteriopathy in vascular EDS and then on the right hand side is our paper…

動脈瘤・解離の管理 ~解離とは~

Vascular Surgery 1:55-3:27 Dissection on the other hand is different. Dissection means that there's a tear in the wall of the artery or the aorta and blood then flows between those layers and what that does is then as you can see in the pi…

動脈瘤・解離の管理 ~動脈瘤とは~

Vascular Surgery 0:18-1:52 Basically my goal for the audience here is to learn the difference between aneurysms and dissections because frequently people can confuse the two. I will show you the distribution of the arterial pathology in va…

運動に関するアドバイス

LDS Guidelines: Then vs. Now 1:21:13-1:24:12 Q:Last question for you, Dr Dietz. In terms of exercising what are your suggestions in terms of kind of like heart rate recommendations or kind of what guidelines say and how you think or feel a…

骨と関節について

LDS Guidelines: Then vs. Now 1:17:49-1:20:45 Q:If anyone has any thoughts on just osteoporosis or joint degradation we might see in Loeys-Dietz syndrome and any type of supplement in terms of calcium or things like that? LDSで見られる骨粗…

吸入ステロイドについて

LDS Guidelines: Then vs. Now 1:16:18-1:17:26 Q:There are few questions about the use of inhalers and flovent and albuterol, which is kind of in your realm, too. Can you address that? フルタイドやサルブタモールなどの吸入ステロイドについて、…

LDSでは自己免疫疾患を起こしやすいか?

LDS Guidelines: Then vs. Now 1:13:55-1:16:15 Q:Any evidence of prevalence of autoimmune conditions with Loeys-Dietz syndrome like rheumatoid arthritis or other immunity, I guess, autoimmune conditions? LDSでは、関節リウマチのような自己免疫…