Entries from 2019-11-01 to 1 month
Loeys Dietz Syndrome: Virtual Medical Symposium Series (11/8/18) 14:21-15:57 Now I'm going to go through some of the physical features and I'll stress when a physical feature only helps us in making the diagnosis and also when a physical f…
Loeys Dietz Syndrome: Virtual Medical Symposium Series (11/8/18) 11:25-14:20 Now Loeys-Dietz syndrome is a condition that we first recognized and described about 13 years ago, back in 2005. ロイス・ディーツ症候群は、およそ13年前の2005年に…
Loeys Dietz Syndrome: Virtual Medical Symposium Series (11/8/18) 6:58-11:24 So that led us to the concept that a special class of blood-pressure medications called angiotensin receptor blockers, with one prominent example being losartan, m…
Loeys Dietz Syndrome: Virtual Medical Symposium Series (11/8/18) 5:43-6:59 Now many different experiments taught us that these microfibrils that are composed of fibrillin-1 serve a second important function in that they normally control th…
As many of you know, Marfan syndrome is a connective tissue disorder that's related to Loeys-Dietz syndrome. It shows features in the eye, in the skeleton and also in the cardiovascular system. 皆さんの多くはご存知だと思いますが、マルファ…
Loeys Dietz Syndrome: Virtual Medical Symposium Series (11/8/18) 2:01-2:48 Good evening, everyone! It's really a pleasure to be you. What I'd like to try to do today is to give you a comprehensive overview of Loeys-Dietz syndrome, but also…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 41:34-42:15 So take care of your aorta by doing the following. Get a routine evaluation by imaging, know and remember your aortic size and have that followed, take medic…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 40:49-41:33And then finally it's important to recognize after a dissection, this is a Type B dissection, the aorta will grow over time. That's a natural history and it h…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 39:41-40:49 The surgery of an aortic dissection involves replacing the aorta with a graft. 大動脈解離の手術では、大動脈を人工血管で置き換えます。 But not with an endogra…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 38:54-39:41The symptom of a dissection is usually abrupt severe chest pain or back pain, something that's never had before. Sharp and severe are the most typical adjecti…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 37:30-38:53 Finally, what is an aortic dissection? What does it feel like? This is a intraoperative example of an aortic dissection provided by Joe Bavaria from Pennsylv…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 36:08-37:29 In Loeys-Dietzs syndrome, we recommend the aorta be operated between4 and 4.5 cm depending on the specific mutation, the family history, the gender, craniofa…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 34:34-36:07 In those caveats are as follows. So it's not strictly a line in the sand, and we often choose an aortic dimension a little less than 5 cm and we start thinki…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 33:26-34:33When should one have aortic surgery? In general, in Marfan and related disorders, once the aorta achieves 5 cm, it's recommended to have prophylactic surgery.…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 30:50-33:25Pregnancy is a risk factor for aortic dissection in women who have Marfan and other genetic aortic conditions. Most of the information we have about that risk…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 29:40-30:48 It's important to recognize that being on a medication for the aorta such as a beta blocker, which slows the heart rate and lessens, lessens force of contrac…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 26:31-29:40When you think about exercise and physical activity, of course, they're different whether you're doing leisurely walking, which would be a dynamic or isotonic…
2018年4月25日 Dominga Noe 私はすごくポジティブな人間―特にマルファン症候群に関してはそうありたいと思っています。この考えにたどり着くまでには長い時間がかかりました。毎日が幸せというわけではありません。でもトータルで見れば、マルファン症候群は…
2018年2月27日Kacey Lamphier 2月は心臓月間ということで、私にとっては特別重要な月です。私は30年間マルファン症候群と共に生きてきましたが、診断を受けたのは22年前です。私は日々マルファン症候群についての自らの体験や知識を広げる活動をしています。…
2019年2月11日 Sarah E. McMillan はじめに 思春期と慢性疾患 自覚 アイデンティティとマルファン 受容とマルファン 医療とQOL はじめに 自分の病気のことを話題にしたくなくて、新しい友達の輪に入って、少し（orメチャクチャ）喋り過ぎたことはありません…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 25:05-26:30 Taking care of your aorta; knowledge is power, so know about your condition. Everybody with Marfan or a related disorder should know they have the condition,…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 23:41-25:04 And unfortunately, it's so fortunately, it is helpful, but it's, it has not been yet proven in the largest trials to be better than beta blocker in single tr…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 22:30-23:40 So in a Marfan mouse, losartan, by blocking TGF-β, improved the aorta. So this wild-type means a normal mouse and between these arrowheads is a normal aortic…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 20:29-22:30 And research from many investigators throughout the world, particularly the group at Johns Hopkins, have demonstrated that there's more to it than just blood…
はじめに ロイス・ディーツ症候群の有病率 ロイス・ディーツ症候群の特徴 ロイス・ディーツ症候群の原因 遺伝について ロイス・ディーツ症候群の診断 正確な診断が重要である理由 ロイス・ディーツ症候群の管理方法 心臓・血管 骨・関節 アレルギー・消化器 …
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 18:20-20:28 One of the basic concepts in medical management, in other words, non-surgical therapy of aortic aneurysm disease, we'll talk about medications, learning abou…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 15:39-18:19 Now, how often should I have a or take imaging and it really depends on the condition, the size of the aorta, and how would, how rapidly it's growing. So for…
はじめに マルファン症候群で一般的にみられる心血管疾患 大動脈拡張・大動脈瘤 大動脈解離 僧帽弁逸脱 大動脈弁逆流 心不全 マルファン症候群で一般的な心血管疾患の管理法 薬 検査 日常生活で注意すべきこと 緊急事態（例：大動脈解離）にすべきこと はじ…
はじめに マルファン症候群における一般的な心臓外科手術の種類 大動脈基部に対する一般的な心臓外科手術の術式 コンポジットグラフト手術（ベントール術） メリット デメリット 自己弁温存術 メリット デメリット 生体弁置換術 メリット デメリット 動脈内…
Taking Care of Your Aorta 10/15/18 (Virtual Medical Symposium Series) 13:22-15:38 This is a CT scan with contrast lighting up the ascending aorta and descending aorta in a person with a very large thoracic aneurysm, this large circle here.…
