海外マルファン情報

米国マルファン症候群患者団体The Marfan Foundationからの情報を中心に、マルファン症候群や関連疾患についての海外情報を翻訳して発信します。

循環器

ERにおける大動脈解離の診断と治療 ~大動脈解離の原因~

Diagnosis and Treatment of Aortic Dissection in the ER (Parts 1 and 2) 5:25-6:34 Why does an aortic dissection occur? What individuals are at risk? First, disorders that lead to abnormalities of the aortic wall. So looking at the microstru…

ERにおける大動脈解離の診断と治療 ~疫学と病態生理~

Diagnosis and Treatment of Aortic Dissection in the ER (Parts 1 and 2) 4:38-5:23 Incidence is about two to six per hundred thousand patients and two-thirds are male with a mean age of about 60 to 65 years old with type A dissections being …

ERにおける大動脈解離の診断と治療 ~大動脈解離の分類~

Diagnosis and Treatment of Aortic Dissection in the ER (Parts 1 and 2) 4:00-4:37 When we think about aortic dissections we want to know what's the onset or origin, where's the location of the dissection and it's classified as type A when t…

ERにおける大動脈解離の診断と治療 ~大動脈解離・大動脈壁内血腫・大動脈穿通性アテローム潰瘍~

Diagnosis and Treatment of Aortic Dissection in the ER (Parts 1 and 2) 2:32-3:59 A classic aortic dissection again is a tear in the aortic wall, so blood then enters into this false channel separated by the intimal flap. The dissection typ…

ERにおける大動脈解離の診断と治療 ~急性大動脈疾患~

Diagnosis and Treatment of Aortic Dissection in the ER (Parts 1 and 2) 1:42-2:31 When we think of acute aortic syndromes aortic dissection is the most classic and is responsible for 80 to 90 percent and in this cross section of the aortic …

ERにおける大動脈解離の診断と治療 ~大動脈解離とは~

Diagnosis and Treatment of Aortic Dissection in the ER (Parts 1 and 2) 0:03-1:40 Hello, my name is Alan Braverman and today we'll discuss what is aortic dissection and who is at risk. This is part of the aortic diseases awareness week lect…

全身の動脈系

はじめに 頭部から頚部にかけての動脈系 胸部・腹部・下肢の動脈系 はじめに 瘤や解離、蛇行は大動脈や動脈系でみられます。本文書は血管系を理解する上での解剖学上の手引書となっています。 頭部から頚部にかけての動脈系 .tg {border-collapse:collapse;b…

大動脈手術を終えた皆さんからのアドバイス

はじめに 執刀医にどのような質問をしましたか? 手術に向けてどのような準備をしましたか? 手術前の検査などについて教えてください -大動脈人工弁の種類はどのように決めましたか? 手術や手術からの回復期について事前に知っておきたかったことはどのよ…

ロイス・ディーツ症候群が疑われる症例での大動脈手術の判断について

What’s in Your LDS Family Tree? Genetics, Variability, Outcomes (September 1, 2020) 58:16-1:01:46 So say that there is someone who has an aortic root or ascending aneurysm, there's no known family history, their genetic testing has thus fa…

妊婦における胸腹部動脈瘤

Marfan Syndrome Management: Back to Basic 54:40-56:43 Can we go back to the abdominal aortic aneurysm for a second? How does that affect pregnancy, what would be your recommendation for that if somebody has an aortic aneurysm, an abdominal…

平均寿命に到達するために必要なこと

Marfan Syndrome Management: Back to Basic 45:16-47:28 Can each of you talk about life, life expectancy, you know, whether somebody's diagnosed early, you know, what, what's the impact on life expectancy from aortic surgery? Question about …

経過観察中の運動と術後の運動について

Marfan Syndrome Management: Back to Basic 42:13-45:13 There are several questions about physical activity and Marfan syndrome and Loeys-Dietz, so Dr. Morris, can you just talk about that from, you know, from diagnosis and while you're moni…

マルファン症候群をはじめから ~大動脈基部以外の心臓手術~

38:06-39:46 There's other considerations that your surgeon is going to talk to you about when thinking about any cardiac surgery for Marfan syndrome. The first is how much aorta to replace. If only the aortic roots is affected then the pat…

マルファン症候群をはじめから ~外科手術の目安となる動脈瘤の大きさ~

Marfan Syndrome Management: Back to Basic 30:21-32:32 Surgery is recommended when the aneurysm is measured at 5.0 centimeters and this is very well accepted guideline by both the Americans and the Europeans, the American College of Cardiol…

マルファン症候群をはじめから ~大動脈解離~

Marfan Syndrome Management: Back to Basic 28:09-30:19 The goal of surgery when you see us is to prevent aortic dissections. There's two times that you're going to meet a cardiac surgeon: one is electively in clinic and we can have small ta…

マルファン症候群をはじめから ~大動脈基部~

Marfan Syndrome Management: Back to Basic 26:12-28:05 The aorta is the largest vessel in the body. It accepts blood from the heart and distributes it to the rest of the body. On the left side is the normal aorta. It's spinning because this…

マルファン症候群をはじめから ~外科手術の準備~

Marfan Syndrome Management: Back to Basic 23:29-26:08 I've been asked to talk about what you need to know about cardiac surgery. My name is Chris Malaisrie. I'm a cardiac surgeon at Northwestern Memorial hospital, a professor of surgery at…

マルファン症候群をはじめから ~画像検査・薬物治療・予防的大動脈置換~

Marfan Syndrome Management: Back to Basic 16:31-19:13 So what can we do to prevent bad outcomes in Marfan syndrome? How can we manage this, how can, how have we changed the life expectancy from 30 to near normal? では、Marfan症候群で最悪の…

マルファン症候群をはじめから ~大動脈瘤vs大動脈解離vs大動脈破裂~

Marfan Syndrome Management: Back to Basic 13:18-16:30 So I'm going to go a little more into the difference between an aneurysm, a rupture, and a dissection, so just looking at this. This is a diagram of the body so as I mentioned here's th…

マルファン症候群をはじめから ~心臓の所見~

Marfan Syndrome Management: Back to Basic 11:39-13:17 And then we'll get to the heart. This is my main area of expertise and interest and the two most common problems in Marfan syndrome are dilation of parts of the aorta and something call…

大動脈手術後のリスク

Living with Risk 56:30-57:36 Several people are asking about risks after aortic surgery so Juan, do you want to talk about that from the aortic point of view? 大動脈手術後のリスクについてもいくつか質問が寄せられています。Juan先生、大動脈の…

大動脈解離の徴候

Living with Risk 46:08-51:26 I want to start with one thing that kept coming up in some of the questions that even were submitted the last couple days and this is about the worry about when is an emergency, in emergency. I mean let me tell…

リスクと生きる ~動脈瘤ができる場所と手術タイミング~

Living with Risk 25:40-28:31 Now what about aneurysms in other locations and what about the timing of surgery? 動脈瘤ができる場所と手術タイミングについての質問です。 This is a complicated slide and but just the main point here is this. So …

リスクと生きる ~自己弁温存術後の大動脈解離B型の発症リスク~

Living with Risk 21:57-23:09 So now here are some questions from participants in today's session. では、本日の参加者の方から寄せられた質問に回答していきたいと思います。 So "Following a valve-sparing procedure, how likely is it to develop o…

リスクと生きる ~小児における大動脈解離発症率~

Living with Risk 15:33-18:03 And we do know that aortic dissection is a rare event. The IRAD registry data note that this occurs in about two to three per 100,000 people and this was a majority male and majority older crowd. 大動脈解離が稀…

リスクと生きる ~マルファン小児の心血管イベントに関する研究~

Living with Risk 3:56-7:10 As, as Eileen and Michael both mentioned I'm a pediatric cardiologist and I've spent really my career in training with Dr. Denver Sallee and then developed an interest in aortic disease and have been involved in …

運動に関するオンライン座談会 ~運動中の大動脈解離の発症率~

Personal Perspectives Panel: Physical Activity & Exercise 16:31-18:40 Thankfully dying suddenly when you're an athlete is very, very rare so it's a rare phenomenon in general and of that rare complication only two percent of death in athle…

運動に関するオンライン座談会 ~大動脈に問題がある場合~

Personal Perspectives Panel: Physical Activity & Exercise 7:33-8:21 And then the aorta is different in everyone. On the slide to your left, next slide, will have an arrow pointing to the aorta in someone that looks normal so that's a norma…

大動脈弓手術について ~弓部の分類~

Surgery Series: Aortic Arch (2/22/21) 17:37-19:01 Obviously you can't just have normal. Normal is normally a three vessel arch branching pattern. 大動脈弓が正常でない場合もあります。正常な大動脈弓とは、弓部から3本血管が出ており、それらから…

大動脈弓手術について ~大動脈の役割~

Surgery Series: Aortic Arch (2/22/21) 11:59-14:19 And obviously with connective tissue disorder patients Dr. Roselli showed slides like this so I’m gonna go over this pretty quickly. With normal aortic wall it's very organized and therefor…