海外マルファン情報

米国マルファン症候群患者団体The Marfan Foundationからの情報を中心に、マルファン症候群や関連疾患についての海外情報を翻訳して発信します。

循環器

Science in Paris からの報告(大動脈疾患) ~大動脈解離サバイバーが望んでいること~

Aortic Disease Research (9/19/22) 20:42-23:20 So, this was a very interesting analysis. Sherene Shalhub and others led a large group of patients to try to understand from patients and families, what, what are the research priorities that y…

大動脈の画像検査 ~CTでみる大動脈解離~

Aortic Imaging: Your Questions Answered 13:28-14:14 The other image I want to share here is how does a dissection look on CT. So this is basically what we call a snake view of the aorta, whole of the aorta. On the top is the root as you co…

大動脈の画像検査 ~造影CTでの上行大動脈の太さ計測~

Aortic Imaging: Your Questions Answered 12:15-13:27 This is a important point I want to make. How is an ascending aorta right above the root is measured? On the left here is a normal technique that's used very often where you measure the a…

大動脈の画像検査 ~CT・造影CT~

Aortic Imaging: Your Questions Answered 10:05-12:14 Then the next technique I want to show are images of thoracic aorta but remember how the tissue is looking here. This is a non-contrast CT so there is no contrast that we have administere…

大動脈の画像検査 ~TTE・TOE~

Aortic Imaging: Your Questions Answered 8:54-10:04 So here, this is where I, the most important part of that presentation is I just want to share images and go over what I'm looking at, so these are echocardiography images on patients on s…

大動脈の画像検査 ~各種画像検査についての説明~

Aortic Imaging: Your Questions Answered 7:05-8:54 With that, you know, the other thing to remember is there are different techniques available. Each has its strength and weaknesses so which to use when it becomes very important. では画像検…

大動脈の画像検査 ~大動脈の部位説明~

Aortic Imaging: Your Questions Answered 6:07-7:01 This is a cartoon showing different areas of the aorta that everybody is interested in knowing that the part that's connected to the heart, the sinus is called basically sinus of valsalva a…

大動脈の画像検査 ~はじめに~

Aortic Imaging: Your Questions Answered 4:44-6:06 Thank you for joining and I would like to thank the Marfan Foundation for giving me an opportunity to present on cardiovascular imaging, especially vascular imaging, which is very important…

大動脈解離が外科手術なしで治ることがあるか?

Advances in the Treatment of Aortic Dissection 56:12-57:53 Q: Does the dissection ever heal so that surgery isn't necessary or does it stabilize, does it ever heal? Eileen: 大動脈解離が自然に治って手術が不要になったり、安定するということは…

大動脈解離手術後の画像検査について

Advances in the Treatment of Aortic Dissection 54:46-56:09 Q: And I'm on the other end, Dr. Ohman, you talked about long-term surveillance after the surgery, so how frequently with what kind of imaging, you know, what do you recommend for …

大動脈解離の前兆はあるか?

Advances in the Treatment of Aortic Dissection 53:56-54:46 Q: People want to know, I mean, they see obviously that it's better to have surgery prophylactically than emergently. Besides the size, which they would know themselves, are there …

ステントグラフト治療が結合組織疾患患者に向かない理由

Advances in the Treatment of Aortic Dissection 44:03-46:55 Q:Dr. Ohman, you mentioned, you said that but the endovascular repair not being for connective tissue disorder patients. There's so many questions about that. Can you explain why a…

大動脈解離の治療における進展 ~B型解離のまとめ~

Advances in the Treatment of Aortic Dissection 40:40-42:15 So where are we going in the future and what, if you take away four things from this talk what should it be? ではまとめです。このスライドにある4つのポイントを覚えておいていただきた…

大動脈解離の治療における進展 ~血管内治療(マルファン関連疾患患者の場合)~

Advances in the Treatment of Aortic Dissection 37:01-40:39 Most of the experiences in the literature are single study or single center institution reports with a handful, maybe, two dozen at best and you can see for patients in both dissec…

大動脈解離の治療における進展 ~血管内治療(一般患者の場合)~

Advances in the Treatment of Aortic Dissection 35:32-37:01 And why is that? So endovascular repair sounds so much better than a big open operation. It's two needle pokes in the groin, you're watched in the ICU but we really have to ask, go…

大動脈解離の治療における進展 ~選択的修復における標準治療(GenTACの声明)~

Advances in the Treatment of Aortic Dissection 34:04-35:31 And so I have to be clear. GenTAC has a statement and, and this is true for patients who are stable and are undergoing elective repair open surgery remains the gold standard. GenTA…

大動脈解離の治療における進展 ~B型解離の手術タイミング~

Advances in the Treatment of Aortic Dissection 31:53-34:04 So when do we make the decision to go to the operating room? If it's an acute, malperfusion issue with solely a type B and they're relatively stable I want to be very clear ―― the …

大動脈解離の治療における進展 ~薬物療法~

Advances in the Treatment of Aortic Dissection 31:12-31:52 Medication remains the gold standard. Nothing has changed. That's true for type A. That's true for type B as well as residual dissections after type A repair. 薬物療法は大動脈解離…

大動脈解離の治療における進展 ~B型解離と妊娠・出産~

Advances in the Treatment of Aortic Dissection 29:12-31:11 What about pregnancy? This is a very common question and we presume that these females who are pregnant are at a higher risk due to the physiologic changes. The heart has to work h…

大動脈解離の治療における進展 ~プレシジョン・メディスンに向けて~

Advances in the Treatment of Aortic Dissection 26:58-29:11 So there's this question of the Phenotype-Genotype interplay. We know that certain gene mutations within the Marfan family are associated with a higher rate of ectopia lentis or sk…

大動脈解離の治療における進展 ~B型解離のリスク因子~

Advances in the Treatment of Aortic Dissection 24:36-26:58 But ultimately what does all of this mean for you, for patients who do have a diagnosis or a suggestion of a genetically triggered aortopathy? B型解離の概要は先程述べた通りですが、…

大動脈解離の治療における進展 ~B型解離の概要~

Advances in the Treatment of Aortic Dissection 22:12-24:35 My name is Wesley Ohman and it's honestly an honor to be paired up with Dr. Moon, who taught me so much about what I'm going to be talking about in terms of management of type B ao…

大動脈解離の治療における進展 ~A型解離治療のまとめ~

Advances in the Treatment of Aortic Dissection 21:01-21:59 So early diagnosis and institution of definitive therapy is the key. A型解離では、早期発見と根本的な治療のできる医療施設で治療を受けられるかどうかがカギとなります。 Surgical treatm…

大動脈解離の治療における進展 ~術後の血圧管理~

Advances in the Treatment of Aortic Dissection 19:51-21:00 These are the couple of most important things. I've got a good friend, Joe Bavaria, who works at the University of Pennsylvania. When we publish these data he told me he keeps this…

大動脈解離の治療における進展 ~治療法別の院内死亡率(IRAD)~

Advances in the Treatment of Aortic Dissection 15:35-16:11 So the IRAD database is a database all over the world that puts all their data into one spot and looks at results. では、IRADからわかっていることをご紹介します。IRADとは、急性大動…

大動脈解離の治療における進展 ~A型解離の手術適応と手術の目的~

Advances in the Treatment of Aortic Dissection 14:06-15:34 So when do we treat an acute dissection? Well, any patient who's deemed survivable and so it used to be that "Oh, if you're over 80 you don't get treated," but that's just not true…

大動脈解離の治療における進展 ~大動脈解離のリスク分類~

Advances in the Treatment of Aortic Dissection 12:43-14:05 If you look at what predicts a problem and if you have an aneurysm your aorta is getting bigger and bigger and bigger. At what point does it become a problem, because it's like a, …

大動脈解離の治療における進展 ~大動脈解離の自然史と死亡原因~

Advances in the Treatment of Aortic Dissection 12:00-12:42 We don't do natural history studies like this anymore because we can treat these patients but this was a study from the late 50s looking at what happened to patients who had dissec…

大動脈解離の治療における進展 ~リスク因子~

Advances in the Treatment of Aortic Dissection 11:27-11:59 Risk factors include the classic patients, a male age 50 to 70, who has hypertension but that's also the typical patient that has a myocardial infarction or a heart attack. 大動脈…

大動脈解離の治療における進展 ~大動脈解離の臨床所見~

Advances in the Treatment of Aortic Dissection 9:40-11:26 The clinical presentation is abrupt onset. I always ask the patient, "When did your pain start?" and they will say, "4:30 when I got, done watching television, went up to go get a b…