海外マルファン情報 | Global Marfan Updates

米国マルファン症候群患者団体The Marfan Foundationからの情報を中心に、マルファン症候群や関連疾患についての海外情報を翻訳して発信します。

Entries from 2025-03-01 to 1 month

血圧正常から低めの患者に対するARBの投与について

Managing HTAD: Key Insights from the 2024 ESC Guidelines 1:07:34-1:10:43 Q: Is the use of ARBs recommended in Marfan patients whose blood pressure is normal to low and this person has a abdominal aneurysm which is followed annually and the…

A型解離とB型解離の違いについて

Managing HTAD: Key Insights from the 2024 ESC Guidelines 1:05:34-1:07:24 Q: What’s the difference between a Type B and a Type A dissection and how is it related to pregnancy? A型解離とB型解離の違いについて教えてください。また、妊娠との関係…

ロサルタンの副作用について

Managing HTAD: Key Insights from the 2024 ESC Guidelines 1:03:09-1:05:28 Q: Are there side effects that come from losartan? Julie? ロサルタンの副作用はありますか? A: Yeah, I can go on. Side effects from the main... the main concern is tha…

セリプロロールの代替薬について

Managing HTAD: Key Insights from the 2024 ESC Guidelines 59:57-1:03:02 Q: There is a question here about Celiprolol not being available in the United States, but currently, you can go into a trial with Celiprolol within the United States. …

運動のメリットについて

Managing HTAD: Key Insights from the 2024 ESC Guidelines 57:36-59:55 Q: This family has genetic testing and they are in the VUS category, but they have been affected by aortic aneurysm for three generations, having, aortic aneurysm repair …

画像検査法の違いについて

Managing HTAD: Key Insights from the 2024 ESC Guidelines 53:52-57:21 Q: Can you speak to the pros and cons of MRA versus gated CT for measurements of the aortic root in LDS or whether there is a case for both, for both tests in surveillanc…

上行大動脈の手術閾値について

Managing HTAD: Key Insights from the 2024 ESC Guidelines 51:58-53:39 Q: For ascending aortic aneurysms, do the ESC guidelines take us back from as 5 cm threshold for high-volume regional centers towards 5.5 cm as a recommended threshold, e…

vEDSの特徴について

Managing HTAD: Key Insights from the 2024 ESC Guidelines 45:34-51:49 Q: So this patient is a newly diagnosed with vEDS at 51 years of age and she's asking whether the condition lies dormant or has she had it since birth because she didn't …

2024 ECSガイドラインについて 〜運動〜

Managing HTAD: Key Insights from the 2024 ESC Guidelines 43:29-44:19 I'm looking at physical activity. It is recommended to individualize physical activity. It used to be discouraged; however, we see that in patients with connective tissue…

2024 ECSガイドラインについて 〜ロサルタンと薬物療法について〜

Managing HTAD: Key Insights from the 2024 ESC Guidelines 42:12-43:27 Furthermore, for medical therapy, we advise Losartan, and why is this the case? This was a study done already in 2006, where it was shown that in mice, if you look at the…

2024 ECSガイドラインについて 〜外科手術〜

Managing HTAD: Key Insights from the 2024 ESC Guidelines 38:04-42:10 And you can see this in our guidelines. So surgery is indeed indicated in patients with Marfan syndrome who have aortic root disease with a diameter of 50 millimeters. Th…

2024 ECSガイドラインについて 〜MFS、LDS、vEDSの違い〜

Managing HTAD: Key Insights from the 2024 ESC Guidelines 33:45-38:03 So first I would like to share some differences between Marfan syndrome, Loeys-Dietz syndrome and Ehlers-Danlos syndrome, which I will get back to later. 私からはまず、MF…

2024 ECSガイドラインについて 〜妊娠・出産〜

Managing HTAD: Key Insights from the 2024 ESC Guidelines 29:24-32:57 To end, I would like to spend a few words on pregnancy because we also have some recommendations there. Data on pregnancy and heritable thoracic aortic disease so far hav…