海外マルファン情報

米国マルファン症候群患者団体The Marfan Foundationからの情報を中心に、マルファン症候群や関連疾患についての海外情報を翻訳して発信します。

循環器

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~ロイス・ディーツ症候群患者の場合~

49:01-50:02 So to conclude I would also make some, some discuss some aspects of pregnancy in patients with Loeys-Dietz syndrome although the data is much scarcer in this group and of course we know that the risk of aortic dissection during…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~妊娠中の心血管手術~

Family Planning and Pregnancy: US and Europe Perspectives 44:57-47:34 So I will continue with the final part of my presentation and discuss surgery during pregnancy and of course this is something we want to avoid but unfortunately still i…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~妊娠中の心エコー・MRI・CT検査~

Family Planning and Pregnancy: US and Europe Perspectives 43:50-44:56 So all our patients with aortic disease should be seen on a regular basis throughout the pregnancy for evaluating the aortic root and echocardiography is the preferred d…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~現行のガイドラインによる治療の転帰~

Family Planning and Pregnancy: US and Europe Perspectives 42:24-43:49 So does it pay off? Well, there are a few studies who actually evaluated the safety and the course of pregnancy in patients who are treated according to the current guid…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~妊娠中の服薬~

41:21-42:23 So one of the previous speaker already discussed the use of the prophetic use of beta blocks in pregnancy. Well, some studies actually observed a reduced rate of progression of aortic dilatation, so according to the European gu…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~妊娠中の画像検査~

Family Planning and Pregnancy: US and Europe Perspectives 39:56-41:20 So patients with aortic pathology should be overseen in specialized centers and supervised by both cardiologists and obstetricians who are actually aware of the potentia…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~妊娠中の血行動態変化~

Family Planning and Pregnancy: US and Europe Perspectives 38:42-39:55 So there is an increased risk for aortic dissection in pregnancy, which is the result of both hemodynamic, hormonal but also from thromboembolic changes and actually pre…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~医療チーム~

Family Planning and Pregnancy: US and Europe Perspectives 37:12-38:41 I will continue this webinar with the next topic, "the follow-up during pregnancy," so in the coming minutes I will discuss when we should see our patients and who actua…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~循環器科のまとめ~

Family Planning and Pregnancy: US and Europe Perspectives 34:58-36:47 And then to end this presentation I just want to mention that every woman wanting to become pregnant should have a cardiac ultrasound done prior to pregnancy to look at …

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~前向き研究のデータからわかること~

Family Planning and Pregnancy: US and Europe Perspectives 34:13-34:57 So very briefly some prospective data and I'm going to skip this slide because I know that Martijn is going to address this one but I just want to mention with you that …

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~大動脈基部置換手術後のリスク~

Family Planning and Pregnancy: US and Europe Perspectives 32:58-34:12 So even after aortic root replacement because if you recommend replacement before pregnancy you should be aware that you are still not in an absolutely safe zone, so the…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~予防的大動脈基部手術の基準値~

Family Planning and Pregnancy: US and Europe Perspectives 29:49-32:57 So how can we reduce the risk? As I mentioned knowing the diagnosis is really, really paramount. Pre-pregnancy counseling as Melissa has nicely explained. Follow-up duri…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~リスク推定~

Family Planning and Pregnancy: US and Europe Perspectives 28:52-29:49 So how can this risk be estimated? We use risk estimations and this is the most widely used risk estimation. The, WHO risk estimation where you have categories going fro…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~大動脈解離のリスク因子~

Family Planning and Pregnancy: US and Europe Perspectives 26:21-28:53 So risk factors in the setting of, of, of Marfan disease and related heritable thoracic aortic diseases diagnosis of the aortopathy is really crucial. Most women in seri…

妊娠・出産について(アメリカ・ヨーロッパの専門医の視点から) ~大動脈解離のリスク~

Family Planning and Pregnancy: US and Europe Perspectives 22:52-26:21 I will be addressing firstly what is the risk that we are talking about, how can we estimate the risk, how can we reduce the risk and I'll be addressing prophylactic sur…

大動脈疾患に関する研究報告(Science in Paris) ~二尖大動脈弁~

Aortic Disease Research (9/19/22) 34:55-38:43 So bicuspid aortic valve is a very common inherent disorder of the aortic valve and a certain percentage of patients 10 to 35 percent also have an abnormal, abnormal aorta. I think it's estimat…

大動脈疾患に関する研究報告(Science in Paris) ~大動脈解離サバイバーが望んでいること~

Aortic Disease Research (9/19/22) 20:42-23:20 So, this was a very interesting analysis. Sherene Shalhub and others led a large group of patients to try to understand from patients and families, what, what are the research priorities that y…

大動脈の画像検査 ~CTでみる大動脈解離~

Aortic Imaging: Your Questions Answered 13:28-14:14 The other image I want to share here is how does a dissection look on CT. So this is basically what we call a snake view of the aorta, whole of the aorta. On the top is the root as you co…

大動脈の画像検査 ~造影CTでの上行大動脈の太さ計測~

Aortic Imaging: Your Questions Answered 12:15-13:27 This is a important point I want to make. How is an ascending aorta right above the root is measured? On the left here is a normal technique that's used very often where you measure the a…

大動脈の画像検査 ~CT・造影CT~

Aortic Imaging: Your Questions Answered 10:05-12:14 Then the next technique I want to show are images of thoracic aorta but remember how the tissue is looking here. This is a non-contrast CT so there is no contrast that we have administere…

大動脈の画像検査 ~TTE・TOE~

Aortic Imaging: Your Questions Answered 8:54-10:04 So here, this is where I, the most important part of that presentation is I just want to share images and go over what I'm looking at, so these are echocardiography images on patients on s…

大動脈の画像検査 ~各種画像検査についての説明~

Aortic Imaging: Your Questions Answered 7:05-8:54 With that, you know, the other thing to remember is there are different techniques available. Each has its strength and weaknesses so which to use when it becomes very important. では画像検…

大動脈の画像検査 ~大動脈の部位説明~

Aortic Imaging: Your Questions Answered 6:07-7:01 This is a cartoon showing different areas of the aorta that everybody is interested in knowing that the part that's connected to the heart, the sinus is called basically sinus of valsalva a…

大動脈の画像検査 ~はじめに~

Aortic Imaging: Your Questions Answered 4:44-6:06 Thank you for joining and I would like to thank the Marfan Foundation for giving me an opportunity to present on cardiovascular imaging, especially vascular imaging, which is very important…

大動脈解離が外科手術なしで治ることがあるか?

Advances in the Treatment of Aortic Dissection 56:12-57:53 Q: Does the dissection ever heal so that surgery isn't necessary or does it stabilize, does it ever heal? Eileen: 大動脈解離が自然に治って手術が不要になったり、安定するということは…

大動脈解離手術後の画像検査について

Advances in the Treatment of Aortic Dissection 54:46-56:09 Q: And I'm on the other end, Dr. Ohman, you talked about long-term surveillance after the surgery, so how frequently with what kind of imaging, you know, what do you recommend for …

大動脈解離の前兆はあるか?

Advances in the Treatment of Aortic Dissection 53:56-54:46 Q: People want to know, I mean, they see obviously that it's better to have surgery prophylactically than emergently. Besides the size, which they would know themselves, are there …

ステントグラフト治療が結合組織疾患患者に向かない理由

Advances in the Treatment of Aortic Dissection 44:03-46:55 Q:Dr. Ohman, you mentioned, you said that but the endovascular repair not being for connective tissue disorder patients. There's so many questions about that. Can you explain why a…

大動脈解離の治療における進展 ~B型解離のまとめ~

Advances in the Treatment of Aortic Dissection 40:40-42:15 So where are we going in the future and what, if you take away four things from this talk what should it be? ではまとめです。このスライドにある4つのポイントを覚えておいていただきた…

大動脈解離の治療における進展 ~血管内治療(マルファン関連疾患患者の場合)~

Advances in the Treatment of Aortic Dissection 37:01-40:39 Most of the experiences in the literature are single study or single center institution reports with a handful, maybe, two dozen at best and you can see for patients in both dissec…