海外マルファン情報

米国マルファン症候群患者団体The Marfan Foundationからの情報を中心に、マルファン症候群や関連疾患についての海外情報を翻訳して発信します。

心血管手術

大動脈弓手術の術中死亡率について

Surgery Series: Aortic Arch (2/22/21) 1:00:24-1:01:28 Q:And so and just going back to that brain perfusion right near the end of your talk. You said that mortality was lower if that was done but you didn't give any numbers. People are aski…

大動脈弓部の手術時間について

Surgery Series: Aortic Arch (2/22/21) 58:03-1:00:23 Q:How long does that surgery take the aortic arch surgery or does it matter which one of, the ones that you showed us. It looks like it looks complicated. 大動脈弓部の手術にはどのくらいの…

大動脈弓部の手術適応について

Surgery Series: Aortic Arch (2/22/21) 56:17-58:02 Q:So, you know, you talked a lot about the need for aortic arch surgery after somebody presented with dissection. Unless so if it was prophylactic surgery but what are the indications for t…

大動脈弓手術について ~反回神経麻痺~

Surgery Series: Aortic Arch (2/22/21) 50:50-52:34 And with that the left recurrent laryngeal nerve, which hopefully you guys can see this pointer, but off the vaso, vegus the left recurrent laryngeal nerve wraps around the arch and it usua…

大動脈弓手術について ~術後管理~

Surgery Series: Aortic Arch (2/22/21) 49:05-50:49 Obviously in the post-op setting there's a variety of things that we're looking for. 術後に確認すべき項目は様々です。 We obviously need a monitor for bleeding when we get up to the ICU. We …

大動脈弓手術について ~抗凝固管理~

Surgery Series: Aortic Arch (2/22/21) 47:25-49:04 As in medicine there's, if there's something good there's always some bad to it so the colder you go the bigger problems you have with bleeding because the proteins that form coagulation or…

大動脈弓手術について ~脳モニタリング~

Surgery Series: Aortic Arch (2/22/21) 46:41-47:23 So cerebral monitoring is crucial to achieve our task and that is there's a variety. 大動脈弓部の手術において、脳のモニタリングは極めて重要であり、様々な検査法を用いて行われます。 There's B…

大動脈弓手術について ~右腋窩動脈灌流~

Surgery Series: Aortic Arch (2/22/21) 45:31-46:40 One of the ways we can do that, as we showed, is the right axillary perfusion so this is where we're instilling flow usually through a graft from the heart-lung machine. 先ほど順行性脳灌流…

大動脈弓手術について ~順行性脳灌流と逆行性脳灌流~

Surgery Series: Aortic Arch (2/22/21) 43:38-45:29 But hypothermia is not the end-all and be-all. You need adjuncts and adjunct is perfusion to the brain and this is a concept that we've has been around and this is kind of like religion in …

大動脈弓手術について ~低体温循環停止法~

Surgery Series: Aortic Arch (2/22/21) 41:09-43:36 So back to the original question, "Why is arch surgery different?" Well, we're balancing perfusion to the heart as well as blood flow to the brain and then blood flow to the rest of the bod…

大動脈弓手術について ~大動脈解離B型を2度起こした19歳Marfan男性の症例~

Surgery Series: Aortic Arch (2/22/21) 39:13-41:07 Here's a picture and some video of a 19-year-old Marfan's patient, who came in a while ago. He had a root aneurysm that hadn't been operated and you can see his initial presentation was a t…

大動脈弓手術について ~フローズン・エレファント・トランク法~

Surgery Series: Aortic Arch (2/22/21) 37:36-39:12 The sun procedure so this is, you know, one thing that's talked about in the aortic community and I gotta say it's a common procedure that a lot of us do for aortic dissections. How that's …

大動脈弓手術について ~エレファント・トランク法~

Surgery Series: Aortic Arch (2/22/21) 35:44-37:35 The elephant trunk procedure, this is, this is important for our connective tissue disorder patients, especially Marfan’s and Loeys-Dietzs where they, they have risk for intervention on the…

大動脈弓手術について ~大動脈弓部置換術の種類~

Surgery Series: Aortic Arch (2/22/21) 33:27-35:42 So with that let's talk a little bit about aortic arch surgery specifically. So there's several different types of arch procedures. I just wanted to make it simpler for everyone so that you…

大動脈弓手術について ~Loeys-Dietz症候群とMarfan症候群における大動脈弓への介入に関する比較研究~

Surgery Series: Aortic Arch (2/22/21) 30:12-33:26 In May of this year Dr. Cameron and his colleagues presented a very interesting study and this compared the Loeys-Dietz patients with Marfan's patients. This is a busy slide but we're going…

大動脈弓手術について ~基部置換初回手術での大動脈弓全置換に関する研究②~

Surgery Series: Aortic Arch (2/22/21) 27:11-30:11 The second study, this was with Dr. Bechet and his colleagues in France. So the purpose was to assess the prevalence, indications, and results of aortic arch replacement in Marfan's patient…

大動脈弓手術について ~基部置換初回手術での大動脈弓全置換に関する研究①~

Surgery Series: Aortic Arch (2/22/21) 24:39-27:10 So one of the questions that kind of comes around in our surge-community is "Should surgeons address the aortic arch at the time of the first operation?" or the index operation. We're going…

大動脈弓手術について ~大動脈解離A型の標準的修復法~

Surgery Series: Aortic Arch (2/22/21) 23:11-24:37 So I'd say can, for conventional type A repair when we look at the data from the STS most surgeons are really doing a supra-coronary anastomosis and then what we call a open distal, in the …

大動脈弓手術について ~大動脈解離A型と大動脈弓~

Surgery Series: Aortic Arch (2/22/21) 20:41-23:10 So with that we can really focus on some of the acute issues so obviously aortic dissection. With classifications there's the DeBakey classification and the Stanford. では、急性疾患である大…

大動脈弓手術について ~手術適応の条件~

Surgery Series: Aortic Arch (2/22/21) 19:02-20:40 So why would a person need an aortic arch surgery? This is actually a picture of one of our Marfan's patients, who had had a previous root procedure and she has a very large abnormal arch a…

大動脈弓手術について ~大動脈弓手術の変遷~

Surgery Series: Aortic Arch (2/22/21) 15:52-17:36 So of course we have to talk about history and the first arch aneurysm resection was actually in 1950 in Paris. It was a 20 year old girl, who came in they thought she had tuberculosis beca…

大動脈弓手術について ~通常の心臓手術~

Surgery Series: Aortic Arch (2/22/21) 14:20-15:50 Obviously to understand why arch surgery is different we've got to understand what normal is. Here's a schematic of a heart potentially in the operating room where we have a cannula in the …

大動脈弓手術について ~はじめに~

Surgery Series: Aortic Arch (2/22/21) 9:43-10:28 Just as a quick outline we'll go over a little introduction. We'll go over some anatomy, some history, we'll look at indications for surgery, we'll go over some concepts that we use in the o…

胸腹部大動脈手術後15年以降の生存率について

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 1:03:08-1:03:57 Q:Any mortality data past 15 years? 紹介していただいた研究では、手術後15年以降の生存率はどうなっていますか? A:Yeah, we have patients that are 20 and 25 years out. We j…

大動脈全置換後の運動について

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 1:01:36-1:02:48 Q:How about in terms of your lifestyle. If somebody has their entire aorta replaced and they have Marfan syndrome does that mean that they can return to "normal" she sa…

大動脈基部と腹部大動脈の同時手術は可能か?

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 56:28-57:25 Q:For patients with both, both a compromised aortic root and an abdominal aneurysm is it possible to do the root replacement at the same time as the abdominal aortic repair…

胸腹部大動脈の置換範囲はどう決めるのか?

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 54:00-56:27 Q:How do you determine how much of the, of the thoracoabdominal aorta to replace? If, if it is all aneurysmal but not all, not all at the surgical threshold you replace at …

真腔と偽腔の大きさの比率は手術タイミングや手術結果に影響するか?

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 51:51-53:58 Q:Does the relative size of the true and false lumen have any impact on surgical thresholds and surgical outcomes? 大動脈での真腔と偽腔の大きさの比率は、手術を検討する基準…

真腔と偽腔の大きさの比率は手術タイミングや手術結果に影響するか?

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 51:51-53:58 Q:Does the relative size of the true and false lumen have any impact on surgical thresholds and surgical outcomes? 大動脈での真腔と偽腔の大きさの比率は、手術を検討する基準…

胸腹部大動脈手術からの回復について

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 48:36-50:10 Q:After the surgery what's the recovery like? How long does the pain last? 手術後の回復までの経過と術後の痛みが続く期間について教えて下さい。 A:It's, it's very different fr…