海外マルファン情報

米国マルファン症候群患者団体The Marfan Foundationからの情報を中心に、マルファン症候群や関連疾患についての海外情報を翻訳して発信します。

心血管手術

胸腹部大動脈瘤の自覚症状と手術を検討するタイミングについて

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 47:38-48:31 Q:You talked a lot about the size of the aneurysm and how you're watching it and what the size would be and you mentioned something about symptoms. What would symptoms be i…

胸腹部大動脈手術の手術時間はどのくらいか?

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 47:17-47:35 Q:First of all that's a huge rep, that's a huge surgery. How long does that take the entire abdominal repair? 非常に大掛かりな手術ですが、胸腹部大動脈の修復完了までどのくら…

胸腹部大動脈手術の手術時間はどのくらいか?

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 47:17-47:35 Q:First of all that's a huge rep, that's a huge surgery. How long does that take the entire abdominal repair? 非常に大掛かりな手術ですが、胸腹部大動脈の修復完了までどのくら…

開胸・開腹術による胸腹部大動脈の修復 ~ステントグラフト~

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 41:44-44:54 I'm going to end by just mentioning endovascular stent grafting with regards to the aorta because we hear so much about it these days. 最後に、大動脈に内挿するステントグラ…

開胸・開腹術による胸腹部大動脈の修復 ~様々な研究結果~

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 36:41-41:13 This is from a paper we wrote a few years ago, looking at 127 patients with thoracoabdominal aortic aneurysm repair, looking at just patients with Marfan syndrome, just pat…

開胸・開腹術による胸腹部大動脈の修復 ~リバースド・エレファント・トランク法~

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 35:44-36:40 On occasion the descending thoracic aorta is symptomatic and large and has to be replaced first but we know we're going to have to go back and do the ascending aorta so we …

開胸・開腹術による胸腹部大動脈の修復 ~エレファント・トランク法~

32:56-35:43 Patients with Marfan syndrome can have ascending, arch, and thoracoabdominal repair and require multiple procedures to have this done and more often than not it's done as a staged operation. Marfan症候群の患者さんの場合、上行大…

開胸・開腹術による胸腹部大動脈の修復 ~人工血管の分枝と各動脈との吻合~

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 30:46-32:57 So now we've moved the cross clamp down onto the graft, restoring flow into these intercostal arteries, which is perfusing the spinal cord and then we do the distal anastom…

開胸・開腹術による胸腹部大動脈の修復 ~大動脈弓と人工血管との吻合~

dOpen Thoracoabdominal Repair: Surgery Series (2/16/21) 27:16-30:45 Once we isolate the aorta approximately between clamps we essentially create a single lumen by removing that wall between the true and the false lumen that we talked about…

開胸・開腹術による胸腹部大動脈の修復 ~左心バイパス~

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 25:37-27:14 We use left heart bypass, so what you see here is drainage from the heart into a centrifugal pump, which then leads blood back into the lower body that allows us to place c…

開胸・開腹術による胸腹部大動脈の修復 ~脳脊髄液ドレナージ~

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 24:26-25:37 We use CSF drainage to reduce the instance of paraplegia. If you look at the Cochrane review from a few years ago all three of the randomized clinical trials were done by o…

開胸・開腹術による胸腹部大動脈の修復 ~切開範囲~

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 22:49-24:25 So let's talk about thoracoabdominal aortic aneurysm repair. Replacing that much of the aorta places a great deal of the body at risk: spinal cord, the kidneys, the bowel, …

開胸・開腹術による胸腹部大動脈の修復 ~修復を検討する胸腹部大動脈のサイズ~

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 20:56-22:48 Most of patients with Marfan syndrome, thoracoabdominal aneurysm, chronic aortic dissection when it comes to the thoracoabdominal aorta, most of them have Type II thoracoab…

開胸・開腹術による胸腹部大動脈の修復 ~マルファン症候群と大動脈手術~

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 18:54-20:55 Most patients with Marfan syndrome undergoing actually thoracoabdominal repair have usually had a prior replacement of the aortic root, not always but the majority of them …

開胸・開腹術による胸腹部大動脈の修復 ~マルファン患者で胸腹部大動脈の修復が必要なケース~

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 15:35-16:48 Most of what I'm going to talk about tonight as I mentioned is really this area from the left subclavian artery down to the bifurcation of the aorta down to the iliac arter…

開胸・開腹術による胸腹部大動脈の修復 ~大動脈基部置換術~

Open Thoracoabdominal Repair: Surgery Series (2/16/21) 12:04-15:32 The idea of aortic repair in surgery is to perform a repair before the aorta gets so large or so weak that it does rupture, so you want to prevent the rupture and prevent t…

大動脈手術後の生活についてのオンライン座談会 ~下行大動脈手術からの回復(医師の解説)~

Personal Perspectives Panel: Life After Aortic Surgery 51:52-53:30 David, is, is recovery harder for somebody who is, who has surgery for the descending aortic aneurysm than what, these folks have had, there's a similar experience? David先…

大動脈手術後の生活についてのオンライン座談会 ~術後の体の不調への対処法①(医師の解説)~

Personal Perspectives Panel: Life After Aortic Surgery 31:17-34:17 So David, some people actually asked, I mean, a lot of great questions but some people said, "Well what if you don't listen to your doctor's orders and what if you don't do…

大動脈手術後の生活についてのオンライン座談会 ~手術後の運動(医師の解説)~

Personal Perspectives Panel: Life After Aortic Surgery 21:42-24:39 I want to go to David for the next question. A lot of people asked about going back to exercise after their operation and after recovery or during recovery or what could th…

大動脈手術後の生活についてのオンライン座談会 ~術後のメンタルヘルス~

Personal Perspectives Panel: Life After Aortic Surgery 14:29-19:06 You know, so some people asked about the mental, the mental process as well. It's not just physical recovery and also as you move on in your life but, you know, during this…

大動脈手術後の生活についてのオンライン座談会 ~手術からの回復(医師の解説)~

Personal Perspectives Panel: Life After Aortic Surgery 11:35-14:28 Everybody sounds pretty similar. David, what do you tell patients about what to expect and what they can do to help their recovery? 皆さん、術後については同じような経験をさ…

Marfan関連疾患におけるCOVID最新情報 ~COVID感染後の心血管手術~

COVID-19 Update for the Marfan, Loeys-Dietz, and VEDS Community 24:22-25:28 This is actually an important topic that came up in one of my patients recently, who was a young person with Marfan syndrome, who was preparing to have an aortic o…

大動脈手術後の生活についてのオンライン座談会 ~回復までの経過~

Personal Perspectives Panel: Life After Aortic Surgery 8:32-11:34 So let me, let me get to our panelists, so what was, what was let's start with right after surgery, what was recovery like for you, were you, were you tired for a long time,…

大動脈手術後の生活についてのオンライン座談会 ~手術年齢について(医師の解説)~

Personal Perspectives Panel: Life After Aortic Surgery 5:58-8:26 Now we're going to go to David and I'm not going to ask you how old you are but we want to get a little we're going to lay the foun... では、David先生に話を伺いたいと思います…

大動脈手術後の生活についてのオンライン座談会 ~手術と年齢~

Personal Perspectives Panel: Life After Aortic Surgery 3:49-5:56 So Hi, everyone. I'm Peter. I am, I had my first surgery planned a month after I graduated high school, so I was 18 at the time. I had it down at Boston Children's Hospital. …

大動脈手術後の生活についてのオンライン座談会 ~パネリスト紹介~

Personal Perspectives Panel: Life After Aortic Surgery 2:37-3:48 So tonight we have five panelists, who are amazing. では、今夜参加していただく5名の素晴らしいパネリストの方をご紹介します。 As Michael said, we have Dr. David Liang, who's a …

マルファン症候群やロイス・ディーツ症候群では必ず大動脈の手術が必要か?

Aortic Root Surgery in Connective Tissue Conditions - Surgery Series (2/10/21) 1:05:42-1:06:33 Q:So do all, do all patients with Marfan or Loeys-Dietz need aortic surgery? マルファン症候群やロイス・ディーツ症候群の患者さんは必ず大動脈の手…

低侵襲手術およびステントについて

Aortic Root Surgery in Connective Tissue Conditions - Surgery Series (2/10/21) 1:04:17-1:05:41 Q:What about but you mentioned stents, what about stents or minimally invasive surgery with the connective tissue patients that we're talking ab…

PEARSの可能性について

Aortic Root Surgery in Connective Tissue Conditions - Surgery Series (2/10/21) 1:02:05-1:04:17 Q:We did talk about the PEARS up to here a little bit. Before Helene did put in the chat box a link to a big presentation that we had last year …

人工弁の種類について

Aortic Root Surgery in Connective Tissue Conditions - Surgery Series (2/10/21) 1:00:10-1:02:04 Q:I know you talked about the different types of valves what's the lifespan of the different valve type, what lasts the longest and what would y…